Utilize este identificador para referenciar este registo: http://hdl.handle.net/10400.10/1806
Título: A Case Report of Nonvasculitic Autoimmune Inflammatory Meningoencephalitis with Sensory Ganglionopathy: A Rare Presentation of Sjögren Syndrome
Autor: Peres, J
Cruz, S
Oliveira, R
Santos, L
Valverde, A
Palavras-chave: Sjogren's syndrome
Síndrome de Sjogren
Peripheral nervous system diseases
Data: 2017
Editora: Hindawi Pub. Corp
Citação: Case Rep Neurol Med. 2017;2017:5696512
Resumo: A 68-year-old Caucasian female was admitted to the emergency department with a progressive history of behavioural symptoms and anxiety followed by visual and auditory hallucinations, forgetfulness, and impaired gait in the previous 3 months. On examination she was psychotic and had a postural and rest tremor of the upper limbs, cogwheel rigidity of the four limbs, retropulsion on standing position, and inability to walk. During the following 2 weeks she developed xerostomia and unilateral parotiditis that improved with steroids. A simultaneous improvement of the cognitive abilities allowed for the detection of sensory ataxia of the lower limbs. Sensory ganglionopathy was then detected with electrophysiological studies. A diagnosis of Sjögren syndrome was suspected and confirmed by salivary gland scintigraphy, Schirmer's test, and submaxillary gland biopsy. We report a case of Sjögren syndrome associated with central and peripheral nervous system involvement, without sicca symptoms preceding the neurological clinical picture. The coexistence of ganglionopathy and a favourable response to immunosuppression are key features that can lead to the correct diagnosis in cases with atypical CNS symptoms, mimicking a rapidly progressive dementia.
Peer review: yes
URI: http://hdl.handle.net/10400.10/1806
DOI: 10.1155/2017/5696512
ISSN: 2090-6676
Versão do Editor: https://www.ncbi.nlm.nih.gov/pmc/articles/PMC5274670/pdf/CRINM2017-5696512.pdf
Aparece nas colecções:NEU - Artigos
ANPAT - Artigos

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